Amyloid-beta precursor protein
Also known as: A4, AD1, APP
Function
Functions as a cell surface receptor and performs physiological functions on the surface of neurons relevant to neurite growth, neuronal adhesion and axonogenesis. Interaction between APP molecules on neighboring cells promotes synaptogenesis. Involved in cell mobility and transcription regulation through protein-protein interactions. Can promote transcription activation through binding to APBB1-KAT5 and inhibits Notch signaling through interaction with Numb. Couples to apoptosis-inducing pathways such as those mediated by G(o) and JIP. Inhibits G(o) alpha ATPase activity (By similarity). Acts as a kinesin I membrane receptor, mediating the axonal transport of beta-secretase and presenilin 1 (By similarity). By acting as a kinesin I membrane receptor, plays a role in axonal anterograde transport of cargo towards synapses in axons. Involved in copper homeostasis/oxidative stress through copper ion reduction. In vitro, copper-metallated APP induces neuronal death directly or is potentiated through Cu(2+)-mediated low-density lipoprotein oxidation. Can regulate neurite outgrowth through binding to components of the extracellular matrix such as heparin and collagen I and IV. The splice isoforms that contain the BPTI domain possess protease inhibitor activity. Induces a AGER-dependent pathway that involves activation of p38 MAPK, resulting in internalization of amyloid-beta peptide and leading to mitochondrial dysfunction in cultured cortical neurons. Provides Cu(2+) ions for GPC1 which are required for release of nitric oxide (NO) and subsequent degradation of the heparan sulfate chains on GPC1.
Classification
- Family (Pfam)
- PF10515 APP_amyloid, PF12924 APP_Cu_bd, PF12925 APP_E2, PF02177 APP_N, PF03494 Beta-APP, PF00014 Kunitz_BPTI
- InterPro
- Amyloid_Cu-bd_sf, Amyloid_glyco, Amyloid_glyco_Abeta, Amyloid_glyco_Abeta_sf, Amyloid_glyco_Cu-bd, Amyloid_glyco_E2_domain, Amyloid_glyco_extra, Amyloid_glyco_heparin-bd, Amyloid_glyco_heparin-bd_sf, Amyloid_glyco_intracell_CS, APP_amyloid_C, APP_CUBD_CS, E2_sf, Kunitz_BPTI, Kunitz_BPTI_sf, PH-like_dom_sf, Prtase_inh_Kunz-CS
- Functional cluster
- Mur-Ligase Peptidoglycan Biosynthesis Enzymes
Experimental structures · PDB · 240
- 1AAP X-ray 1.50A
- 1AMB NMR
- 1AMC NMR
- 1AML NMR
- 1BA4 NMR
- 1BA6 NMR
- 1BJB NMR
- 1BJC NMR
- 1BRC X-ray 2.50A
- 1CA0 X-ray 2.10A
- 1HZ3 NMR
- 1IYT NMR
- … and 228 more
A predicted model is available from AlphaFold.
Gene Ontology · 125
- GO:0106003 amyloid-beta complex
- GO:0097449 astrocyte projection
- GO:0030424 axon
- GO:0009986 cell surface
- GO:0005905 clathrin-coated pit
- GO:0005737 cytoplasm
- GO:0005829 cytosol
- GO:0030425 dendrite
- GO:0043198 dendritic shaft
- GO:0043197 dendritic spine
- GO:0005769 early endosome
- GO:0031901 early endosome membrane
- GO:0005783 endoplasmic reticulum
- GO:0005788 endoplasmic reticulum lumen
- GO:0005768 endosome
- GO:0031904 endosome lumen
- GO:0070062 extracellular exosome
- GO:0005576 extracellular region
- GO:0005615 extracellular space
- GO:0005794 Golgi apparatus
- GO:0005796 Golgi lumen
- GO:0005798 Golgi-associated vesicle
- GO:1990812 growth cone filopodium
- GO:1990761 growth cone lamellipodium
- GO:0044304 main axon
- GO:0016020 membrane
- GO:0045121 membrane raft
- GO:0005743 mitochondrial inner membrane
- GO:0098992 neuronal dense core vesicle
- GO:0005641 nuclear envelope lumen
- GO:0043204 perikaryon
- GO:0048471 perinuclear region of cytoplasm
- GO:0005886 plasma membrane
- GO:0031093 platelet alpha granule lumen
- GO:0043235 receptor complex
- GO:0055037 recycling endosome
- GO:0045202 synapse
- GO:0043083 synaptic cleft
- GO:0032588 trans-Golgi network membrane
- GO:0003677 DNA binding
- GO:0019899 enzyme binding
- GO:0070851 growth factor receptor binding
- GO:0008201 heparin binding
- GO:0042802 identical protein binding
- GO:0016504 peptidase activator activity
- GO:0120283 protein serine/threonine kinase binding
- GO:0051425 PTB domain binding
- GO:0048018 receptor ligand activity
- GO:0004867 serine-type endopeptidase inhibitor activity
- GO:0030546 signaling receptor activator activity
- GO:0005102 signaling receptor binding
- GO:0046914 transition metal ion binding
- GO:0008344 adult locomotory behavior
- GO:1990000 amyloid fibril formation
- GO:0048143 astrocyte activation
- GO:0002265 astrocyte activation involved in immune response
- GO:0008088 axo-dendritic transport
- GO:0016199 axon midline choice point recognition
- GO:0007409 axonogenesis
- GO:0006816 calcium ion transport
- GO:0007155 cell adhesion
- GO:1904646 cellular response to amyloid-beta
- GO:0071320 cellular response to cAMP
- GO:0071280 cellular response to copper ion
- GO:0071287 cellular response to manganese ion
- GO:1990090 cellular response to nerve growth factor stimulus
- GO:0071874 cellular response to norepinephrine stimulus
- GO:0007417 central nervous system development
- GO:0050890 cognition
- GO:0048669 collateral sprouting in absence of injury
- GO:0016358 dendrite development
- GO:0006897 endocytosis
- GO:0030198 extracellular matrix organization
- GO:0110088 hippocampal neuron apoptotic process
- GO:0006878 intracellular copper ion homeostasis
- GO:0035235 ionotropic glutamate receptor signaling pathway
- GO:0007612 learning
- GO:0007611 learning or memory
- GO:0007626 locomotory behavior
- GO:0007617 mating behavior
- GO:0014005 microglia development
- GO:0001774 microglial cell activation
- GO:0098815 modulation of excitatory postsynaptic potential
- GO:0008285 negative regulation of cell population proliferation
- GO:0010629 negative regulation of gene expression
- GO:1900272 negative regulation of long-term synaptic potentiation
- GO:0031175 neuron projection development
- GO:1990535 neuron projection maintenance
- GO:0016322 neuron remodeling
- GO:0098989 NMDA selective glutamate receptor signaling pathway
- GO:0007219 Notch signaling pathway
- GO:1905908 positive regulation of amyloid fibril formation
- GO:0050850 positive regulation of calcium-mediated signaling
- GO:0032722 positive regulation of chemokine production
- GO:0070374 positive regulation of ERK1 and ERK2 cascade
- GO:0010628 positive regulation of gene expression
- GO:0045821 positive regulation of glycolytic process
- GO:0050729 positive regulation of inflammatory response
- GO:0032731 positive regulation of interleukin-1 beta production
- GO:0032755 positive regulation of interleukin-6 production
- GO:0046330 positive regulation of JNK cascade
- GO:1900273 positive regulation of long-term synaptic potentiation
- GO:0045931 positive regulation of mitotic cell cycle
- GO:1901224 positive regulation of non-canonical NF-kappaB signal transduction
- GO:0051247 positive regulation of protein metabolic process
- GO:0032224 positive regulation of synaptic transmission, cholinergic
- GO:2000406 positive regulation of T cell migration
- GO:0045944 positive regulation of transcription by RNA polymerase II
- GO:0032760 positive regulation of tumor necrosis factor production
- GO:0010468 regulation of gene expression
- GO:0048169 regulation of long-term neuronal synaptic plasticity
- GO:0040014 regulation of multicellular organism growth
- GO:0043523 regulation of neuron apoptotic process
- GO:1905606 regulation of presynapse assembly
- GO:0150003 regulation of spontaneous synaptic transmission
- GO:0050803 regulation of synapse structure or activity
- GO:0006417 regulation of translation
- GO:0030111 regulation of Wnt signaling pathway
- GO:0045471 response to ethanol
- GO:1990418 response to insulin-like growth factor stimulus
- GO:0070555 response to interleukin-1
- GO:0010288 response to lead ion
- GO:0036269 swimming behavior
- GO:0050808 synapse organization
- GO:0008542 visual learning
Disease associations
- Alzheimer disease type 1 MONDO:0007088
- cerebral amyloid angiopathy, APP-related MONDO:0011583
Drugs targeting this protein · 2
- TRAMIPROSATE stabiliser
- VALILTRAMIPROSATE stabiliser
Related proteins · sequence + function similarity
- Amyloid-beta precursor protein 1.00
- Amyloid-beta precursor protein 1.00
- Amyloid-beta precursor protein 1.00
- Amyloid-beta precursor protein 1.00
- Amyloid-beta precursor protein 1.00
- Amyloid-beta precursor protein 0.99
- Amyloid-beta precursor protein 0.99
- Amyloid-beta A4 protein 0.94
- Amyloid-beta A4 protein 0.93
- Amyloid beta precursor like protein 2 0.86
- Amyloid beta precursor like protein 2 0.85
- Amyloid beta precursor like protein 2 0.80
Co-cited proteins · studied together in the literature
- Amyloid-beta precursor protein 5 shared papers
- Amyloid beta precursor protein binding family B member 2 2 shared papers
- Amyloid-beta precursor protein 1 shared papers
- Tumor necrosis factor receptor superfamily member 21 2 shared papers
- Amyloid-beta precursor-like protein 2 shared papers
- Amyloid beta precursor like protein 2 2 shared papers
- Ankyrin repeat and sterile alpha motif domain-containing protein 1B 1 shared papers
- Beta-secretase 2 2 shared papers
- Amyloid-beta A4 precursor protein-binding family B member 3 1 shared papers
- Glypican-1 1 shared papers
- Gamma-secretase-activating protein 1 shared papers
- Gamma-secretase-activating protein 1 shared papers
Literature · 171 cited papers
- Retraction Note: APP binds DR6 to trigger axon pruning and neuron death via distinct caspases. Nature · 2024
- Recognition of the amyloid precursor protein by human gamma-secretase. Science · 2019
- Common fibrillar spines of amyloid-beta and human islet amyloid polypeptide revealed by microelectron diffraction and structure-based inhibitors. J. Biol. Chem. · 2018
- Fibril structure of amyloid-beta(1-42) by cryo-electron microscopy. Science · 2017
- Phosphorylation of amyloid precursor protein by mutant LRRK2 promotes AICD activity and neurotoxicity in Parkinson's disease. Sci. Signal. · 2017
- A Binuclear Zinc Interaction Fold Discovered in the Homodimer of Alzheimer's Amyloid-beta Fragment with Taiwanese Mutation D7H. Angew. Chem. Int. Ed. Engl. · 2017
- Interplay of histidine residues of the Alzheimer's disease Abeta peptide governs its Zn-induced oligomerization. Sci. Rep. · 2016
- A single kinase generates the majority of the secreted phosphoproteome. Cell · 2015
- Abeta promotes VDAC1 channel dephosphorylation in neuronal lipid rafts. Relevance to the mechanisms of neurotoxicity in Alzheimer's disease. Neuroscience · 2014
- Amyloid precursor protein dimerization and synaptogenic function depend on copper binding to the growth factor-like domain. J. Neurosci. · 2014
- Lysosomal sorting of amyloid-beta by the SORLA receptor is impaired by a familial Alzheimer's disease mutation. Sci. Transl. Med. · 2014
- Rare coding variants in the phospholipase D3 gene confer risk for Alzheimer's disease. Nature · 2014
- … and 159 more in the literature graph